As many NMD impact respiratory muscles, monitoring respiratory function is vital. In specialist clinics this is often conducted by the physiotherapist using:

• Forced Vital Capacity (FVC)
• Forced Expiratory Volume / 1 sec (FEV1)
• Peak Cough Flow (PCF).

These may be performed in sitting and lying to identify the relative involvement of the diaphragm. In conjunction with other signs and symptoms a referral may be made to a home ventilation team or other respiratory support provided.

It is also important to assess for symptoms of hypoventilation and establish history of chest infections. This history should include frequency of chest infections, antibiotic use, and any unplanned hospital admissions.

Individuals may have respiratory equipment and a care plan in place.